primary ciliary dyskinesia 44 without situs inversusCILD44
obo:hasOBONamespace
disease_ontology
n4:IAO_0000115
A primary ciliary dyskinesia characterized by recurrent sinopulmonary infections, defective mucociliary clearance, short respiratory epithelial cell motile cilia with decreased motility, and absence of situs inversus that has_material_basis_in homozygous or compound heterozygous mutation in NEK10 on chromosome 3p24.1.