BDPLT5platelet-type bleeding disorder 5factor V Quebec
obo:hasOBONamespace
disease_ontology
n2:IAO_0000115
A blood platelet disease characterized by autosomal dominant inheritance of delayed onset bleeding after challenge, moderate to severe bleeding tendencies, frequent ecchymoses, mucocutaneous bleeding, muscle and joint bleeds and platelet alpha-granule degredation that has material_basis_in heterozygous tandem duplication of the PLAU gene on chromosome 10q22.