Presenile Dementia with Spastic AtaxiaFBDCerebral Amyloid Angiopathy, British TypeFamilial British Dementia
obo:hasOBONamespace
disease_ontology
n2:IAO_0000115
A cerebral amyloid angiopathy characterized by onset in the 4th to 6th decade of life, progressive mental deterioration, spasticity, muscular rigidity but no tremors, spontaneous movements or sensory changes that has_material_basis_in an autosomal dominant mutation of ITM2B on chromosome 13q14.2.