Lethal ataxia with deafness and optic atrophysyndromic X-linked mental retardation 18ARTSfatal X-linked ataxia with deafness and loss of visionMRXS18syndromic X-linked mental retardation Arts typeMRXSARTS
obo:hasOBONamespace
disease_ontology
n2:IAO_0000115
An X-linked disease that is characterized by profound congenital sensorineural hearing impairment, early-onset hypotonia, delayed motor development, mild to moderate intellectual disability, ataxia, and increased risk of infection and has_material_basis_in mutations of the PRPS1 gene.